Herlyn-Werner-Wunderlich syndrome: a case report
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Abstract
Introduction: Herlyn-Werner-Wunderlich syndrome is among Müllerian malformations of the female genital tract, consisting of the association of uterus didelphys, hemivaginal obstruction and ipsilateral renal agenesis. Objective: To discuss this rare syndrome in the setting of investigation of acute pelvic pain in female teenagers. Case Description: We report a case of a patient referred to our hospital, whose clinical and imaging findings were compatible with this syndrome, and the consequences of this anomaly in close follow up. Discussion: This is a rare condition, and its incidence is not reported by the literature, frequently diagnosed during puberty in the clinical setting of pelvic pain caused by the obstruction to the hemivaginal menstrual flow. As menstrual bleeding normally occurs due to the non-obstructed hemivagina, the diagnosis of these patients is often delayed, favoring the development of complications such as pelvic infection, infertility and endometriosis. Treatment is surgical, with removal of the hemivaginal septum and drainage of the obstructed uterine cavity.
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